Leukocyte adhesion deficiency type III
ORPHA:99844· ICD-10 D84.8
Definition
A form of leukocyte adhesion deficiency (LAD) characterized by both severe bacterial infections and a severe bleeding disorder.
- Prevalence
- <1 / 1 000 000
- Inheritance
- Autosomal recessive
- Age of onset
- Childhood, Infancy