VIPoma
ORPHA:97282· ICD-10 D37.7
Definition
VIPoma is an extremely rare type of pancreatic neuroendocrine tumor that secretes vasoactive intestinal polypeptide (VIP) leading to the manifestations of watery diarrhea, hypokalemia and achlorhydia or hypochhlorhydia (known as WDHA syndrome).
- Prevalence
- <1 / 1 000 000
- Inheritance
- Not applicable
- Age of onset
- All ages