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Deafness-infertility syndrome

ORPHA:94064· ICD-10 Q93.5

Definition

Deafness-infertility syndrome (DIS) is a very rare syndrome associating sensorineural deafness and male infertility.

Prevalence
<1 / 1 000 000
Inheritance
Autosomal recessive
Age of onset
Childhood, Infancy, Neonatal