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Classic bladder exstrophy

ORPHA:93930· ICD-10 Q64.1

Definition

A subtype of exstrophy-epispadias complex (EEC) characterized by an open bladder plate, epispadias and an anterior defect of the pelvis, pelvic floor and the abdominal wall.

Prevalence
1-9 / 100 000
Inheritance
Multigenic/multifactorial
Age of onset
Infancy, Neonatal