Immune-mediated thrombotic thrombocytopenic purpura
ORPHA:93585· ICD-10 M31.1
Definition
A rare, non-hereditary thrombotic thrombocytopenic purpura (TTP), characterized by profound peripheral thrombocytopenia, microangiopathic hemolytic anemia (MAHA) and single or multiple organ failure of variable severity.
- Prevalence
- Unknown
- Inheritance
- Multigenic/multifactorial
- Age of onset
- All ages