Zollinger-Ellison syndrome
ORPHA:913· ICD-10 E16.4
Definition
A rare neuroendocrine neoplasm (NEN) characterized by severe peptic disease (ulcers/esophageal disease) caused by hypergastrinemia secondary to a gastrin-secreting NEN (gastrinoma) resulting in increased gastric acid secretion.
- Prevalence
- 1-9 / 1 000 000
- Inheritance
- Not applicable
- Age of onset
- Adult, Elderly