Localized scleroderma
ORPHA:90289· ICD-10 L94.0
Definition
A rare skin disease characterized by inflammatory and sclerosing disease affecting the skin and underlying connective tissues (subcutaneous tissue, fascia, muscle or bone). It causes cutaneous patches or bands of skin inflammation and thickness affecting the head, neck region, trunk and extremities.
- Prevalence
- 1-9 / 100 000
- Inheritance
- Not applicable
- Age of onset
- All ages