Cutaneous small vessel vasculitis
ORPHA:889· ICD-10 M31.0
Definition
A small vessel vasculitis characterized by neutrophilic inflammation predominantly limited to the superficial cutaneous postcapillary venules and without systemic vasculitis or glomerulonephritis. Typical presentation is of unifocal or multifocal palpable purpura on the lower extremities.
- Prevalence
- Unknown
- Inheritance
- Not applicable
- Age of onset
- All ages