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Primary cutaneous peripheral T-cell lymphoma not otherwise specified

ORPHA:86885· ICD-10 C84.4

Definition

An extremely rare, primary cutaneous T-cell lymphoma disorder characterized by solitary, or multifocal and diffuse, cutaneous lesions, ranging from tumor-like patches, plaques, papules, nodules, and/or erythroderma, located on any area of the body, which rapidly progress and may become ulcerated and/or infected. Systemic involvement may be associated.

Inheritance
Not applicable
Age of onset
Adult, Elderly