Systemic-onset juvenile idiopathic arthritis
ORPHA:85414· ICD-10 M08.2
Definition
A rare pediatric rheumatological disease characterized by the variable occurrence of chronic arthritis, intermittent high spiking fever, maculopapular rash during fever episodes, hepatomegaly and/or splenomegaly, lymphadenopathy, and serositis.
- Prevalence
- 1-9 / 100 000
- Inheritance
- Multigenic/multifactorial, Unknown
- Age of onset
- Childhood