vitalwiki

Congenital dyserythropoietic anemia

ORPHA:85· ICD-10 D64.4

Definition

A group of hematologic diseases characterized by impaired late-stage erythropoiesis and abnormal erythroid precursors, leading to chronic anemia of variable severity.

Prevalence
1-9 / 1 000 000
Inheritance
Autosomal dominant, Autosomal recessive, X-linked recessive
Age of onset
Childhood