Mixed connective tissue disease
ORPHA:809· ICD-10 M35.1
Definition
Mixed connective tissue disease (MCTD) is a rare connective tissue disorder combining clinical features of systemic lupus erythematosus (SLE), systemic sclerosis (SSc), polymyositis (PM) and/or rheumatoid arthritis (RA).
- Prevalence
- 1-9 / 1 000 000
- Inheritance
- Multigenic/multifactorial
- Age of onset
- Adolescent, Adult, Childhood