SAPHO syndrome
ORPHA:793· ICD-10 M86.3
Definition
A rare, pyogenic autoinflammatory disease, characterized by the association of neutrophilic cutaneous involvement and chronic nonbacterial osteomyelitis.
- Prevalence
- Unknown
- Inheritance
- Multigenic/multifactorial, Not applicable
- Age of onset
- Adolescent, Adult, Elderly