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Episodic ataxia type 3

ORPHA:79135· ICD-10 G11.8

Definition

A rare form of Hereditary episodic ataxia characterized by vestibular ataxia, vertigo, tinnitus, and interictal myokymia.

Prevalence
<1 / 1 000 000
Inheritance
Autosomal dominant
Age of onset
All ages