Lymphoid interstitial pneumonia
ORPHA:79128· ICD-10 J84.1
Definition
A rare idiopathic interstitial pneumonia characterized by a diffuse, dense, polyclonal lymphoid cell infiltration of the pulmonary interstitium and air spaces, with high prevalence in patients with immune dysregulation. Presenting symptoms are non-specific and include dyspnea and cough. The clinical course is highly variable, ranging from spontaneous resolution to progressive, fatal respiratory failure.
- Prevalence
- Unknown
- Inheritance
- Not applicable
- Age of onset
- All ages