Immunoglobulin A vasculitis
ORPHA:761· ICD-10 D69.0
Definition
A rare, small-vessel vasculitis characterized by skin purpura, arthritis, abdominal and/or renal involvement, IgA tissue deposits (arterioles, capillaries, and venules) and circulating IgA immune complexes.
- Prevalence
- Unknown
- Inheritance
- Not applicable
- Age of onset
- Childhood