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Familial isolated restrictive cardiomyopathy

ORPHA:75249· ICD-10 I42.5

Definition

A rare genetic cardiac disease characterized by restrictive ventricular filling due to high ventricular stiffness that results in severe diastolic dysfunction in the absence of dilated or hypertrophied ventricles.

Prevalence
Unknown
Inheritance
Autosomal dominant, Autosomal recessive, Not applicable
Age of onset
All ages