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Relapsing polychondritis

ORPHA:728· ICD-10 M94.1

Definition

A rare, clinically heterogeneous, multisystemic inflammatory disease characterized by inflammation of the cartilage and proteoglycan rich structures leading to cartilage damage along with joint, ocular and cardiovascular involvement.

Prevalence
1-9 / 1 000 000
Inheritance
Unknown
Age of onset
All ages