CANOMAD syndrome
ORPHA:71279· ICD-10 G61.8
Definition
A rare chronic immune-mediated polyneuropathy characterized by a progressive disabling neuropathy with marked gait disturbance primarily due to sensory ataxia with concurrent cranial neuropathies (internal or external ophthalmoplegia, dysphagia, dysarthria, or facial weakness) and anti-disialosyl IgM antibodies.
- Prevalence
- <1 / 1 000 000
- Age of onset
- Adult, Elderly