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Immunodeficiency due to selective anti-polysaccharide antibody deficiency

ORPHA:70593· ICD-10 D80.8

Definition

A rare primary immunodeficiency characterized by normal immunoglobulin levels (including IgG sub-classes) but impaired polysaccharide responsiveness.

Prevalence
Unknown
Inheritance
Multigenic/multifactorial
Age of onset
Adolescent, Adult, Childhood