Immunodeficiency due to selective anti-polysaccharide antibody deficiency
ORPHA:70593· ICD-10 D80.8
Definition
A rare primary immunodeficiency characterized by normal immunoglobulin levels (including IgG sub-classes) but impaired polysaccharide responsiveness.
- Prevalence
- Unknown
- Inheritance
- Multigenic/multifactorial
- Age of onset
- Adolescent, Adult, Childhood