Bullous pemphigoid
ORPHA:703· ICD-10 L12.0
Definition
A rare autoimmune bullous skin disease characterized by acquired, subepidermal tense bullae occurring on normal of inflamed skin and that is typically widespread (occurring in the flexor regions of the proximal arms and legs, in the armpits, groin and the abdomen) and often associated with pruritus. The evolution is typically chronic with spontaneous exacerbations and remission.
- Prevalence
- 1-9 / 100 000
- Inheritance
- Not applicable
- Age of onset
- All ages