Extracutaneous mastocytoma
ORPHA:66662· ICD-10 C96.2
Definition
A rare neoplastic disease characterized by a localized, unifocal, low-grade tumor composed of mature mast cells, without evidence of systemic mastocytosis or skin lesions. The tumor most commonly arises in the lung and shows a non-destructive growth pattern.
- Prevalence
- <1 / 1 000 000
- Age of onset
- All ages