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Craniorachischisis

ORPHA:63260· ICD-10 Q00.1

Definition

Craniorachischisis is the most severe form of neural tube defect in which both the brain and spinal cord remain open to varying degrees. It is a very rare congenital malformation of the central nervous system.

Inheritance
Multigenic/multifactorial, Not applicable
Age of onset
Infancy, Neonatal