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Familial multiple nevi flammei

ORPHA:624· ICD-10 Q82.5

Definition

Familial multiple nevi flammei is a rare, genetic capillary malformation disorder characterized by dark red to purple birthmarks which manifest as flat, sharply circumscribed cutaneous lesions, typically situated in the head and neck region, in various members of a single family. The lesions grow proportionally with the individual, change in color and often thicken with age.

Inheritance
Autosomal dominant
Age of onset
Neonatal