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Non-syndromic bicoronal and metopic craniosynostosis

ORPHA:620198· ICD-10 Q75.0

Definition

A form of non-syndromic multisutural craniosynostosis characterized by premature fusion of the bicoronal and metopic sutures, resulting in brachycephaly and trigonocephaly.

Prevalence
<1 / 1 000 000
Age of onset
Neonatal