Non-syndromic metopic and sagittal craniosynostosis
ORPHA:620192· ICD-10 Q75.0
Definition
A form of non-syndromic multisutural craniosynostosis characterized by premature fusion of the metopic and sagittal sutures, resulting in trigonocephaly and scaphocephaly but with mild frontal bossing.
- Prevalence
- <1 / 1 000 000
- Age of onset
- Neonatal