Non-syndromic unicoronal and sagittal craniosynostosis
ORPHA:620186· ICD-10 Q75.0
Definition
A form of non-syndromic multisutural craniosynostosis characterized by premature fusion of the unicoronal and sagittal sutures, resulting in anterior plagiocephaly with contralateral frontal bulging and elongated head shape (turricephaly). Orbital abnormality and strabismus are associated features.
- Prevalence
- <1 / 1 000 000
- Age of onset
- Neonatal