Congenital heart block
ORPHA:60041· ICD-10 Q24.6
Definition
Congenital heart block (CHB) is a rare disorder of atrioventricular conduction, characterized by absence of conduction of atrial impulses to the ventricles with slower ventricular rhythm (atrioventricular dissociation). CHB can occur in association with immunological evidence of maternal connective disease (autoimmune CHD), fetal structural CHD or can be idiopathic.
- Prevalence
- 1-9 / 100 000
- Inheritance
- Not applicable
- Age of onset
- Infancy, Neonatal