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Cold agglutinin disease

ORPHA:56425· ICD-10 D59.1

Definition

Cold agglutinin disease is a type of autoimmune hemolytic anemia defined by the presence of cold autoantibodies (autoantibodies which are active at temperatures below 30°C).

Prevalence
1-9 / 1 000 000
Inheritance
Multigenic/multifactorial
Age of onset
Adult