Primary cutaneous lymphoma
ORPHA:542
Definition
A group of rare primary organ-specific lymphoma characterized by heterogeneous T-cell and B-cell non-Hodgkin lymphomas present in the skin. Clinical and pathological features, evolutive profile, prognosis, molecular etiology and response to therapy are highly variable between the entities belong to this group.
- Prevalence
- 1-9 / 1 000 000