Plummer-Vinson syndrome
ORPHA:54028· ICD-10 D50.1
Definition
Plummer-Vinson or Paterson-Kelly syndrome presents as a classical triad of dysphagia, iron-deficiency anemia and esophageal webs.
- Prevalence
- <1 / 1 000 000
- Inheritance
- Unknown
- Age of onset
- Adult