Rare cutaneous lupus erythematosus
ORPHA:535
Definition
Rare cutaneous lupus erythematosus (CLE) is an autoimmune disease that denotes a heterogeneous spectrum of clinical manifestations affecting the skin and can be divided into 4 categories: acute CLE (ACLE); subacute CLE (SCLE); chronic CLE (CCLE; the most diverse form); and intermittent CLE (ICLE). CLE can either occur alone or associated with systemic lupus erythematosus (SLE).
- Prevalence
- 1-5 / 10 000
- Inheritance
- Multigenic/multifactorial
- Age of onset
- All ages