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Hereditary leiomyomatosis and renal cell cancer

ORPHA:523· ICD-10 C64

Definition

Hereditary leiomyomatosis and renal cell cancer (HLRCC) is a hereditary cancer syndrome characterized by a predisposition to cutaneous and uterine leiomyomas and, in some families, to renal cell cancer.

Prevalence
Unknown
Inheritance
Autosomal dominant
Age of onset
Adolescent, Adult, Elderly