Primary effusion lymphoma
ORPHA:48686· ICD-10 C83.8
Definition
Primary effusion lymphoma (PEL) is a large B-cell lymphoma located in the body cavities, characterized by pleural, peritoneal, and pericardial fluid lymphomatous effusions and that is always associated with human herpes virus-8 (HHV-8).
- Prevalence
- <1 / 1 000 000
- Age of onset
- Adult