Linear IgA dermatosis
ORPHA:46488· ICD-10 L10.8
Definition
A rare, acquired autoimmune bullous skin disease characterized by annular, grouped blisters on the skin and, frequently, mucous membranes with linear deposition of immunoglobulin A along the basement membrane zone (BMZ).
- Prevalence
- 1-9 / 1 000 000
- Inheritance
- Not applicable
- Age of onset
- All ages