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Idiopathic spontaneous coronary artery dissection

ORPHA:458718· ICD-10 I25.4

Definition

A rare vascular disease characterized by idiopathic detachment of the layers of the walls of coronary arteries, creating a false lumen which limits the main coronary flow, leading to myocardial ischemia. Clinical manifestations include acute coronary syndromes, especially ST-segment elevation myocardial infarction (STEMI), syncope, cardiogenic shock, or sudden cardiac death. The condition typically affects young women.

Prevalence
Unknown
Inheritance
Not applicable
Age of onset
Adult