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Lambert-Eaton myasthenic syndrome

ORPHA:43393· ICD-10 G73.1

Definition

Lambert-Eaton myasthenic syndrome (LEMS) is an autoimmune, presynaptic disorder of neuromuscular transmission characterized by fluctuating muscle weakness and autonomic dysfunction frequently associated with small-cell lung cancer (SCLC).

Prevalence
1-9 / 1 000 000
Inheritance
Not applicable
Age of onset
Adult