PFAPA syndrome
ORPHA:42642· ICD-10 E85.0
Definition
PFAPA (Periodic fever - aphthous stomatitis- pharyngitis - adenopathy) syndrome is an auto inflammatory syndrome characterized by recurrent febrile episodes associated with aphthous stomatitis, pharyngitis and cervical adenitis.
- Prevalence
- Unknown
- Inheritance
- Unknown
- Age of onset
- Childhood, Infancy