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Wildervanck syndrome

ORPHA:3456· ICD-10 Q87.8

Definition

Wildervanck syndrome is characterized by the triad of cervical vertebral fusion (Klippel-Feil anomaly), bilateral abducens palsy with retracted eyes (Duane syndrome) and congenital perceptive deafness.

Prevalence
<1 / 1 000 000
Age of onset
Infancy, Neonatal