Essential thrombocythemia
ORPHA:3318· ICD-10 D47.3
Definition
Essential thrombocythemia (ET) is a myeloproliferative neoplasm (MPN) characterized by a sustained elevation of platelet number (> 450 x 109/L) with a tendency for thrombosis and hemorrhage.
- Prevalence
- 1-5 / 10 000
- Inheritance
- Multigenic/multifactorial, Not applicable
- Age of onset
- All ages