Sézary syndrome
ORPHA:3162· ICD-10 C84.1
Definition
Sézary syndrome (SS) is an aggressive form of cutaneous T-cell lymphoma characterized by a triad of erythroderma, lymphadenopathy and circulating atypical lymphocytes (Sézary cells).
- Prevalence
- Unknown
- Inheritance
- Multigenic/multifactorial, Not applicable
- Age of onset
- Adult