Dermatofibrosarcoma protuberans
ORPHA:31112· ICD-10 C49.9
Definition
Dermatofibrosarcoma protuberans (DFSP) is a rare infiltrating soft tissue sarcoma, generally of low grade malignancy, arising from the dermis of the skin and characteristically associated with a specific chromosomal translocation t(17;22).
- Prevalence
- 1-5 / 10 000
- Inheritance
- Not applicable
- Age of onset
- All ages