Onychocytic matricoma
ORPHA:300504· ICD-10 D23.9
Definition
A rare, benign, nail tumor originating in the nail matrix characterized by localized pachyonychia and variable degrees of pigmentation: pigmented, melanocytic (common, longitudinal melanonychia that may simulate a foreign body) or hypopigmented. Histopathology demonstrates a purely epithelial tumor with endokeratinization in the deep portion and concentrically arranged nests of prekeratogenous and keratogenous cells.
- Prevalence
- <1 / 1 000 000
- Age of onset
- Adolescent, Adult, Childhood, Elderly