Leukocyte adhesion deficiency
ORPHA:2968· ICD-10 D84.8
Definition
A rare primary immunodeficiency characterized by defects in the leukocyte adhesion process, marked leukocytosis, recurrent infections, and delayed detachment of the umbilical cord.
- Prevalence
- Unknown
- Inheritance
- Autosomal recessive
- Age of onset
- Childhood, Infancy