Idiopathic chronic eosinophilic pneumonia
ORPHA:2902· ICD-10 J82
Definition
A rare, severe, interstitial lung disease characterized by insidious onset with subacute or chronic non-specific respiratory manifestations (dyspnea, cough, wheezing) often associated with systemic manifestations (fatigue, malaise, weight loss) and a history of asthma (up to half of patients). Eosinophilia is present in most cases, usually in excess of 1000 cells/mm3.
- Prevalence
- Unknown
- Inheritance
- Not applicable
- Age of onset
- All ages