Epstein-Barr virus-positive diffuse large B-cell lymphoma
ORPHA:289661· ICD-10 C83.3
Definition
Epstein-Barr virus-positive diffuse large B-cell lymphoma of the elderly is a rare form of diffuse large B-cell lymphoma occurring most commonly in patients over the age of 50 (usually between 70-75 years of age), without overt immunodeficiency, and presenting with nodal and extranodal involvement (in sites such as the stomach, lung, skin and pancreas) and B symptoms (fever, night sweats, weight loss). The tumor is characterized by an aggressive course and a short survival rate.
- Prevalence
- Unknown
- Inheritance
- Not applicable
- Age of onset
- Adult, Elderly