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Juvenile nasopharyngeal angiofibroma

ORPHA:289596· ICD-10 D10.6

Definition

Juvenile nasopharyngeal angiofibroma (JNA) is a rare and benign but locally aggressive fibrovascular tumor arising from the posterolateral wall of the nasopharynx, which affects mainly young and adolescent males (onset usually occurring between 7-19 years of age) and that presents as a mass in the nasopharynx and nasal cavity, leading to manifestations such as nasal obstruction, epistaxis, profound facial swelling, proptosis or diplopia. Although slowly progressive, it has a high rate of recurrence and sometimes invades adjacent structures.

Prevalence
Unknown
Inheritance
Not applicable
Age of onset
Adolescent, Childhood