Hailey-Hailey disease
ORPHA:2841· ICD-10 Q82.8
Definition
A rare, genetic, chronic epidermal disorder characterized by diffuse bilateral (or, rarely, localized segmental) erythematous plaques with blistering, erosions, maceration, and frequent secondary infection involving the flexural areas.
- Prevalence
- Unknown
- Inheritance
- Autosomal dominant
- Age of onset
- Adult