Partial pancreatic agenesis
ORPHA:2805· ICD-10 Q45.0
Definition
Partial agenesis of the pancreas is characterized by the congenital absence of a critical mass of pancreatic tissue.
- Prevalence
- <1 / 1 000 000
- Inheritance
- Autosomal recessive
- Age of onset
- Infancy, Neonatal