Autoimmune pancreatitis type 1
ORPHA:280302· ICD-10 K86.1
Definition
Type 1 autoimmune pancreatitis is a form of autoimmune pancreatitis seen in elderly males (>60 years) and presenting with abdominal pain, steatorrhea, obstructive jaundice and other organ (bile duct, kidneys and retroperitoneum) involvement. It is thought to be due to an immunoglobulin G4 (IgG4)-associated systemic disease.
- Prevalence
- Unknown
- Inheritance
- Not applicable
- Age of onset
- Adult